Developmental Anomalies : Peutz Jheghers Syndrome; Etiology Clinical Features Oral Manifestations and Treatment

CLINICAL FEATURES
The intestinal polyposis is a disease of the intestine. The polyps can be found all over in the intestine but manifest symptomatically only in the small intestine.
The patient frequently complains of abdominal pain. The examination reveals intussusception of the intestine.
ORAL MANIFESTATIONS
The perioral skin shows numerous pigmented spots about 1-5 mm in diameters with greater concentration towards lips and gradually fading at the periphery.
The spots can similarly be concentrated at the eyes and nose also.
Intraorally buccal mucosa is most frequently affected with pigmentation while gingiva and the hard palate follow.
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