Developmental Anomalies : Facial Hemiatrophy Etiology Clinical Features Oral Manifestations Histologic Features and Treatment

FACIAL HEMIATROPHY
Also known as Parry – Romberg Syndrome, Romberg Syndrome or Hemifacial Atrophy.

ETIOLOGY
Trophic malfunction of the cervical sympathetic nervous system

CLINICAL FEATURES
The skin, subcutaneous tissue, muscle and bone show atrophy.
Various cartilages of the face are also involved.
Contralateral Jacksonian epilepsy, trigeminal neuralgia, and changes in the eyes and hair are commonly seen.
There is a marked predilection for the left side of the face.

ORAL MANIFESTATIONS
The intraoral tissues also show atrophic changes.
If the teeth are developing they are also similarly affected showing short crown or roots.

TREATMENT
There is no treatment but the lesion stops progressing after a certain period of time and remains so for the rest of the life.